Ebstein's anomaly and other tricuspid valve anomalies

The tricuspid valve is the largest of the four cardiac valves and is located between the right atrium and right ventricle. The tricuspid valve complex consists of leaflets, the fibrous tricuspid annulus, the chordae tendinae, papillary muscles, and the right atrial and right ventricular myocardium. Tricuspid valve is affected by a wide variety of abnormalities both congenital and acquired. The clinical impact of these abnormalities also varies widely depending upon the lesion and its impact on right heart function. Congenital anomalies of the tricuspid valve are rare, and among all congenital tricuspid valve defects, tricuspid atresia is more common and is usually diagnosed at or soon after birth. Ebstein's anomaly is less common, and due to its variable, clinical presentation may not be diagnosed until adulthood.