Abstract
Wegener's Granulomatosis (WG) is characterized by the clinical triad of upper and lower respiratory disease and renal insufficiency. Because WG masquerades as a syndrome its diagnosis is often delayed. Astute clinicians should include WG in their differential diagnosis when a patient presents with these classic findings. The diagnosis is a clinicopathologic one made by biopsy of appropriate tissue showing necrotizing granulomatous vasculitis. Lung tissue obtained by open thoracotomy has the highest diagnostic yield. At one time a universally fatal illness WG is now treatable with cyclophosphamide and prednisone therapy with remission in most cases. The authors present a case report of a pediatric patient who was eventually diagnosed with WG. The case serves as a reminder to all clinicians to keep this entity as a part of their diagnostic armamentarium.
Original language | English |
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Pages (from-to) | 563-565 |
Number of pages | 3 |
Journal | The Journal of the Oklahoma State Medical Association |
Volume | 96 |
Issue number | 12 |
DOIs | |
State | Published - Dec 2003 |
ASJC Scopus subject areas
- Medicine (all)